L Carnitine in Mitochondria Encyclopedia MDPI Role of Carnitine Shuttle System in the Active Transport of Fatty Acyl Coa into the mitochondrial Mitochondrial transport of long chain fatty acids. While medium and Download Scientific Diagram Carnitine Shuttle an overview ScienceDirect Topics L carnitine is primarily synthesized in the liver from the amino acids lysine and methionine through a series of four enzymatic reactions, with the liver and kidneys converting the precursor butyrobetaine into active